Contents 1 6a. Diseases of the nervous system (320-359) 1.1 inflammatory diseases of the central nervous system (320-327) 1.2 hereditary and degenerative diseases of the central nervous system (330-337) 1.3 pain (338-338) 1.4 Other headache syndromes (339-339) 1.5 other disorders of the central nervous system (340-349) 1.6 disorders of the peripheral nervous system (350-359) 2 See also

[edit] 6a. Diseases of the nervous system (320-359)

[edit] inflammatory diseases of the central nervous system (320-327)

• (320) Bacterial meningitis
  • (320.0) Meningitis, hemophilus
  • (320.9) Meningitis, bacterial, NOS

• (321) Meningitis due to other organisms
  • (321.0) Cryptococcal meningitis

• (322) Meningitis of unspecified cause

• (323) Encephalitis, myelitis, and encephalomyelitis
  • (323.6) Postinfectious encephalitis
  • (323.9) Encephalitis, unspec.

• (324) Intracranial and intraspinal abscess

• (325) Phlebitis and thrombophlebitis of intracranial venous sinuses
  • (325.0) Venous sinus thrombosis, intracranial

• (326) Late effects of intracranial abscess or pyogenic infection

• (327) Sleep disorders
  • (327.00) Organic insomnia, unspecified
  • (327.01) Insomnia due to medical condition classified elsewhere
  • (327.02) Insomnia due to mental disorder

[edit] hereditary and degenerative diseases of the central nervous system (330-337)

• (330) Cerebral degenerations usually manifest in childhood
  • (330.0) Leukodystrophy
    • Krabbe disease
    • Pelizaeus-Merzbacher disease
  • (330.1) Cerebral lipidoses
    • Tay-Sachs disease

• (331) Other cerebral degenerations
  • (331.0) Alzheimer's
  • (331.1) Pick's disease
  • (331.2) Senile degeneration of brain
  • (331.3) Communicating hydrocephalus
  • (331.4) Obstructive hydrocephalus
  • (331.5) Idiopathic normal pressure hydrocephalus
  • (331.8) Other cerebral degeneration
    • (331.81) Reye's syndrome
    • (331.82) Dementia with Lewy bodies
    • (331.83) Mild cognitive impairment, so stated

• (332) Parkinson's disease
  • (332.0) Parkinsonism, primary

• (333) Other extrapyramidal disease and abnormal movement disorders
  • (333.0) Other degenerative diseases of the basal ganglia
    • Olivopontocerebellar atrophy
    • Shy-Drager syndrome
  • (333.1) Essential tremor/familial tremor
  • (333.2) Myoclonus
    • Lafora's disease
    • Unverricht disease
  • (333.4) Huntington's chorea
  • (333.8) Fragments of torsion dystonia
    • (333.81) Blepharospasm
  • (333.9) Other and unspecified extrapyramidal diseases and abnormal movement disorders
    • (333.99) Other extrapyramidal diseases and abnormal movement disorders
      • Restless legs
      • Serotonin syndrome

• (334) Spinocerebellar disease
  • (334.0) Friedreich's ataxia
    • Spinocerebellar ataxia
  • (334.1) Hereditary spastic paraplegia
  • (334.2) Primary cerebellar degeneration
  • (334.3) Other cerebellar ataxia
  • (334.4) Cerebellar ataxia in diseases classified elsewhere
  • (334.8) Other spinocerebellar diseases
    • Ataxia-telangiectasia [Louis-Bar syndrome]
    • Corticostriatal-spinal degeneration
  • (334.9) Spinocerebellar disease unspecified

• (335) Anterior horn cell disease
  • (335.2) Motor neuron disease
    • (335.20) Amyotrophic lateral sclerosis
    • (335.21) Progressive muscular atrophy
    • (335.22) Progressive bulbar palsy
    • (335.23) Pseudobulbar palsy
    • (335.24) Primary lateral sclerosis
    • (335.29) Other motor neuron diseases

• (336) Other diseases of spinal cord
  • (336.0) Syringomyelia and syringobulbia

• (337) Disorders of the autonomic nervous system
  • (337.0) Idiopathic peripheral autonomic neuropathy
    • (337.00) Idiopathic peripheral autonomic neuropathy, unspecified
    • (337.01) Carotid sinus syndrome
    • (337.09) Other idiopathic peripheral autonomic neuropathy
  • (337.1) Peripheral autonomic neuropathy in disorders classified elsewhere
  • (337.2) Reflex sympathetic dystrophy
  • (337.3) Autonomic dysreflexia
  • (337.9) Unspecified disorder of autonomic nervous system

[edit] pain (338-338)

• (338) Pain, not elsewhere classified
  • (338.0) Central pain syndrome
  • (338.1) Acute pain
  • (338.2) Chronic pain
  • (338.3) Neoplasm related pain (acute) (chronic)
  • (338.4) Chronic pain syndrome

[edit] Other headache syndromes (339-339)

• (339) Other headache syndromes
  • (339.0) Cluster headaches and other trigeminal autonomic cephalgias
    • (339.00) Cluster headache syndrome, unspecified
    • (339.01) Episodic cluster headache
    • (339.02) Chronic cluster headache
    • (339.03) Episodic paroxysmal hemicrania
    • (339.04) Chronic paroxysmal hemicrania
    • (339.05) Short lasting unilateral neuralgiform headache with conjunctival injection and tearing
    • (339.09) Other trigeminal autonomic cephalgias
  • (339.1) Tension type headache
    • (339.10) Tension type headache, unspecified
    • (339.11) Episodic tension type headache
    • (339.12) Chronic tension type headache
  • (339.2) Post-traumatic headache
    • (339.20) Post-traumatic headache, unspecified
    • (339.21) Acute post-traumatic headache
    • (339.22) Chronic post-traumatic headache
  • (339.3) Drug induced headache, not elsewhere classified
  • (339.4) Complicated headache syndromes
    • (339.41) Hemicrania continua
    • (339.42) New daily persistent headache
    • (339.43) Primary thunderclap headache
    • (339.44) Other complicated headache syndrome
  • (339.8) Other specified headache syndromes
    • (339.81) Hypnic headache
    • (339.82) Headache associated with sexual activity
    • (339.83) Primary cough headache
    • (339.84) Primary exertional headache
    • (339.85) Primary stabbing headache
    • (339.89) Other headache syndromes

[edit] other disorders of the central nervous system (340-349)

• (340) Multiple sclerosis

• (341) Other demyelinating diseases of central nervous system
  • (341.0) Neuromyelitis optica
  • (341.1) Schilder's disease
  • (341.2) Acute myelitis (transverse myelitis)

• (342) Hemiplegia
  • (342.0) Hemiplegia, flaccid
  • (342.1) Hemiplegia, spastic

• (343) Infantile cerebral palsy
  • (343.0) Cerebral palsy, paraplegic, congenital
  • (343.1) Cerebral palsy, hemiplegic, congenital
  • (343.2) Cerebral palsy, quadriplegic

• (344) Other paralytic syndromes
  • (344.0) Quadraplegia and quadraparesis
  • (344.1) Paraplegia
  • (344.2) Diplegia of upper limbs
  • (344.3) Monoplegia of lower limb
  • (344.4) Monoplegia of upper limb
  • (344.5) Unspecified monoplegia
  • (344.6) Cauda equina syndrome
  • (344.8) Other specified paralytic syndromes
    • (344.81) Locked-in state
  • (344.9) Paralysis unspecified

• (345) Epilepsy
  • (345.0) Epilepsy, absence, w/o intractable epilepsy
  • (345.1) Epilepsy, tonic-clonic, w/o status
  • (345.3) Epilepsy, status
  • (345.4) Epilepsy, temporal lobe, w/o status
  • (345.9) Epilepsy, unspec., w/o status

• (346) Migraine
  • (346.0) Migraine, classical, not intractable
  • (346.1) Migraine, common, not intractable
  • (346.2) Headaches, cluster, not intractable
  • (346.9) Migraine, unspec., not intractable

• (347) Cataplexy and narcolepsy
  • (347.0) Narcolepsy, w/o cataplexy

• (348) Other conditions of brain
  • (348.0) Cerebral cysts
  • (348.1) Anoxic brain damage
  • (348.2) Pseudotumor cerebri
  • (348.3) Encephalopathy, unspec.
    • (348.31) Encephalopathy, metabolic
  • (348.4) Compression of brain
  • (348.5) Cerebral edema

• (349) Other and unspecified disorders of the nervous system
  • (349.0) Headache, post spinal puncture
    • Post dural puncture headache
  • (349.8) Other specified disorders of nervous system
    • (349.81) Cerebrospinal fluid rhinorrhea
    • (349.82) Toxic encephalopathy

[edit] disorders of the peripheral nervous system (350-359)

• (350) Trigeminal nerve disorders
  • (350.1) Trigeminal neuralgia

• (351) Facial nerve disorders
  • (351.0) Bell's palsy

• (352) Disorders of other cranial nerves

• (353) Nerve root and plexus disorders
  • (353.0) Thoracic outlet syndrome
  • (353.6) Phantom limb

• (354) Mononeuritis of upper limb and mononeuritis multiplex
  • (354.0) Carpal tunnel

• (355) Mononeuritis of lower limb
  • (355.0) Lesion of sciatic nerve
  • (355.1) Meralgia paresthetica
  • (355.2) Other lesion of femoral nerve
  • (355.3) Lesion of lateral popliteal nerve
  • (355.4) Lesion of medial popliteal nerve
  • (355.5) Tarsal tunnel syndrome
  • (355.6) Lesion of plantar nerve
    • Morton's neuroma
  • (355.7) Other mononeuritis of lower limb
  • (355.8) Mononeuritis of lower limb unspecified
  • (355.9) Mononeuritis of unspecified site

• (356) Hereditary and idiopathic peripheral neuropathy

• (357) Inflammatory and toxic neuropathy
  • (357.0) Guillain-Barré syndrome
  • (357.5) Neuropathy, poly-, alcoholic
  • (357.9) Neuropathy, poly-, unspec.

• (358) Myoneural disorders
  • (358.0) Myasthenia gravis w/o exacerbation
    • (358.01) Myasthenia gravis w/ exacerbation

• (359) Muscular dystrophies and other myopathies
  • (359.0) Congenital hereditary myopathies, including:
    • Benign congenital myopathy
    • Central core disease
    • Centronuclear myopathy
    • Myotubular myopathy
    • Nemaline body disease
  • (359.1) Muscular dyst., hereditary

[edit] See also

• List of ICD-9 codes
• ICD-10 Chapter G: Diseases of the nervous system

v • d • e Pathology: Medical conditions (Diseases/Disorders/Illness, Syndromes/Sequences, Symptoms/Signs, Injuries, etc.) and ICD codes (A/B, 001-139) Infectious disease/Infection: Bacterial disease (G+, G-) · Virus disease · Parasitic disease (Protozoan infection, Helminthiasis, Ectoparasitic infestation) · Mycosis · Zoonosis (C/D, 140-239 & 280-289) Cancer (C00-D48, 140-239) Tumor Myeloid hematologic (D50-D77, 280-289) Anemia · Coagulopathy Lymphoid immune (D80-D89, 279) Immunodeficiency · Immunoproliferative disorder · Hypersensitivity (E, 240-278) Endocrine disease · Nutrition disorder · Inborn error of metabolism (F, 290-319) Mental disorder (G, 320-359) Nervous system disease (CNS, PNS) · Neuromuscular disease (H, 360-389) Eye disease · Ear disease (I, 390-459) Cardiovascular disease (Heart disease, Vascular disease) (J, 460-519) Respiratory disease (Obstructive lung disease, Restrictive lung disease, Pneumonia) (K, 520-579) Stomatognathic disease (Tooth disease) · Digestive disease (Esophageal, Stomach, Enteropathy, Liver, Pancreatic) (L, 680-709) Skin disease · skin appendages (Nail disease, Hair disease, Sweat gland disease) (M, 710-739) Musculoskeletal disorders · Osteochondropathy (Osteopathy, Chondropathy) (N, 580-629) Urologic disease (Nephropathy, Urinary bladder disease) · Male genital disease · Breast disease · Female genital disease (O, 630-679) Complications of pregnancy · Obstetric labor complication · Puerperal disorder (P, 760-779) Fetal disease (Q, 740-759) Congenital disorder (R, 780-799) Syndromes · Medical signs (Eponymous) (S/T, 800-999) Bone fracture · Joint dislocation · Sprain · Strain · subluxation · Head injury · Chest trauma · Poisoning

v • d • e Diseases of meninges (G00–G03, 320–322) Meningitis/Arachnoiditis: Bacterial (Tuberculous, Haemophilus, Pneumococcal) · Viral (Herpesviral) · Fungal (Cryptococcal) · Aseptic (Drug-induced) Meningoencephalitis central nervous system navs: anat/physio/dev, noncongen/congen/neoplasia, symptoms+signs/eponymous, proc

v • d • e Pathology of the nervous system, primarily CNS (G04–G47, 323–349) Inflammation Brain Encephalitis (Viral encephalitis, Herpesviral encephalitis) · Cavernous sinus thrombosis · Brain abscess (Amoebic) Spinal cord Myelitis: Poliomyelitis · Demyelinating disease (Transverse myelitis) · Tropical spastic paraparesis Both/either Encephalomyelitis (Acute disseminated) Meningoencephalitis Brain/ encephalopathy Degenerative Extrapyramidal and movement disorders Basal ganglia disease: Parkinsonism (PD, Postencephalitic, NMS) · PKAN · Tauopathy (PSP) · Striatonigral degeneration · Hemiballismus · HD · OA Dyskinesia: Dystonia (Spasmodic torticollis, Meige's, Blepharospasm) · Chorea (Choreoathetosis) · Myoclonus (Myoclonic epilepsy) Tremor (Essential tremor, Intention tremor) · Restless legs · Stiff person Dementia Tauopathy: Alzheimer's (Early-onset) · Frontotemporal dementia/Frontotemporal lobar degeneration (Pick's, Dementia with Lewy bodies) Multi-infarct dementia Mitochondrial disease Leigh's Demyelinating autoimmune (Multiple sclerosis, Neuromyelitis optica, Schilder's disease) · hereditary (Adrenoleukodystrophy, Alexander, Canavan, Krabbe, ML, PMD, VWM, MFC, CAMFAK syndrome) · Central pontine myelinolysis · Marchiafava-Bignami disease · Alpers' Episodic/ paroxysmal Seizure/epilepsy Focal · Generalised · Status epilepticus · Myoclonic epilepsy Headache Migraine (Familial hemiplegic) · Cluster · Tension Cerebrovascular TIA (Amaurosis fugax, Transient global amnesia) Stroke (MCA, ACA, PCA, Foville's, Millard-Gubler, Lateral medullary, Weber's, Lacunar stroke) Sleep disorders Insomnia · Hypersomnia · Sleep apnea (Obstructive, Ondine's curse) · Narcolepsy · Cataplexy · Kleine-Levin · Circadian rhythm sleep disorder (Advanced sleep phase syndrome, Delayed sleep phase syndrome, Non-24-hour sleep-wake syndrome, Jet lag) CSF Intracranial hypertension (Hydrocephalus/NPH, Idiopathic intracranial hypertension) · Cerebral edema · Intracranial hypotension Other Brain herniation · Reye's · Hepatic encephalopathy · Toxic encephalopathy Spinal cord/ myelopathy Syringomyelia · Syringobulbia · Morvan's syndrome · Vascular myelopathy (Foix-Alajouanine syndrome) · Spinal cord compression Both/either Degenerative SA Friedreich's ataxia · Ataxia telangiectasia MND UMN only: PLS · PP · HSP LMN only: PMA · PBP (Fazio-Londe, Infantile progressive bulbar palsy) · SMA (SMN-linked, Kennedy disease, SMAX2, DSMA1) both: ALS central nervous system navs: anat/physio/dev, noncongen/congen/neoplasia, symptoms+signs/eponymous, proc

v • d • e Psychophysiology: Sleep (G47, 327) Sleep stages Rapid eye movement sleep · Non-rapid eye movement sleep · Slow-wave sleep Brain waves Alpha wave · Beta wave · Gamma wave · Delta wave · Theta rhythm · K-complex Sleep disorders Dyssomnia Insomnia · Narcolepsy · Sleep apnea (Obesity hypoventilation syndrome, Ondine's curse) · Hypersomnia · Circadian rhythm sleep disorder (Advanced sleep phase syndrome, Delayed sleep phase syndrome, Non-24-hour sleep-wake syndrome, Jet lag) Parasomnia Night terror · Sleepwalking · Somniloquy Other/ungrouped Night eating syndrome · Nocturia · Nocturnal myoclonus · Sleep deprivation Benign phenomena Dream · Exploding head syndrome · False awakening · Hypnagogia · Hypnic jerk · Lucid dream · Nightmare · Nocturnal emission · Nocturnal Penile Tumescence · Sleep paralysis · Somnolence Related topics Bed (Bunk bed, Four poster bed, Futon, Hammock, Mattress) · Bed bug · Bedding · Bedroom · Bedtime · Bedtime toy · Bedtime story · Caffeine nap · Chronotype · Dream journal · Hypnopompic state · Lullaby · Methods of falling asleep · Nap · Nightwear · Polyphasic sleep · Polysomnography · Power nap · Siesta · Sleep and creativity · Sleep and learning · Sleep debt · Sleep diary · Sleep inertia · Sleep medicine · Sleeping while on duty · Sleepover · Snoring · Excessive daytime sleepiness · ("Sleeping sickness", which is not a sleep disorder.)

v • d • e Autonomic diseases, Dysautonomia, autonomic- neuropathy (G90, 337) HSAN I · II · III/Familial dysautonomia · IV/Congenital insensitivity to pain with anhidrosis · V Orthostatic intolerance Postural orthostatic tachycardia syndrome · Orthostatic hypotension Other Horner's syndrome · Multiple system atrophy · Pure autonomic failure · Autonomic dysreflexia peripheral nervous system navs: anat/histo/physio/dev, noncongen PNS somatic/autonomic/congen/neoplasia, symptoms+signs/eponymous, proc

v • d • e CNS disease: Headache (G43-G44, 339, 346) Primary ICHD 1 Migraine (Familial hemiplegic) · Retinal migraine ICHD 2 Tension ICHD 3 Cluster · Chronic paroxysmal hemicrania ICHD 4 Hemicrania continua · Thunderclap headache · Coital cephalalgia · New daily persistent headache · Hypnic headache Secondary ICHD 7 Ictal headache · Post dural puncture headache ICHD 8 Hangover · Medication overuse headache ICHD 13 Trigeminal neuralgia · Occipital neuralgia · External compression headache · Cold-stimulus headache · Optic neuritis · Postherpetic neuralgia · Tolosa-Hunt syndrome Other Vascular central nervous system navs: anat/physio/dev, noncongen/congen/neoplasia, symptoms+signs/eponymous, proc

v • d • e Multiple sclerosis and other demyelinating diseases of CNS (G35–G37, 340–341) Signs and symptoms Ataxia · Depression · Diplopia · Dysarthria · Dysphagia · Fatigue · Incontinence · Neurological fatigue · Nystagmus · Optic neuritis · Pain · Uhthoff's phenomenon · Dawson's fingers Diagnosis and evolution following McDonald criteria · Poser criteria · EDSS · Clinically isolated syndrome Investigation Pathophysiology · Experimental autoimmune encephalomyelitis Treatment Interferon · Glatiramer acetate · Mitoxantrone · Natalizumab · Therapies under investigation Borderline forms Acute disseminated encephalomyelitis · Balo concentric sclerosis · Neuromyelitis optica · Guillain-Barré syndrome · Marburg multiple sclerosis · Schilder's disease · Tumefactive multiple sclerosis Other List of people with multiple sclerosis · List of multiple sclerosis organizations

v • d • e Cerebral palsy and other paralytic syndromes (G80-G83, 342-344) Paresis and plegia NOS Paralysis · Quadriplegia · Triplegia · Hemiplegia/Hemiparesis · Paraplegia/Diplegia · Monoplegia Flaccid vs. spastic Upper motor neuron lesion: Spastic diplegia · Spastic paraplegia (Hereditary spastic paraplegia) Lower motor neuron lesion: Flaccid paralysis Specific types Cerebral palsy · Cauda equina syndrome · Locked-in syndrome central nervous system navs: anat/physio/dev, noncongen/congen/neoplasia, symptoms+signs/eponymous, proc

v • d • e Nervous system pathology, PNS, Somatic (G50–G64, 350–357) Nerve, nerve root, plexus Cranial nerve disease V (Trigeminal neuralgia) · VII (Facial nerve paralysis, Bell's palsy, Melkersson–Rosenthal syndrome, Central seven) · XI (Accessory nerve disorder) Radiculopathy, plexopathy brachial plexus (Brachial plexus lesion, Thoracic outlet syndrome) · Phantom limb Mono- neuropathy Upper limb median nerve (Carpal tunnel syndrome, Ape hand deformity) ulnar nerve (Ulnar nerve entrapment, Froment's sign, Guyon's canal syndrome, Ulnar claw) radial nerve (Radial neuropathy, Wrist drop) long thoracic nerve (Winged scapula) Lower limb lateral cutaneous nerve of thigh (Meralgia paraesthetica) tibial nerve (Tarsal tunnel syndrome) plantar nerve (Morton's neuroma) superior gluteal nerve (Trendelenburg's sign) sciatic nerve (Piriformis syndrome) General Causalgia · Mononeuritis multiplex · Neuropathy (Neuralgia/Neuritis) Polyneuropathies/ Polyradiculoneuropathy HMSN Charcot-Marie-Tooth disease · Dejerine Sottas syndrome · Refsum's disease · Hereditary spastic paraplegia Autoimmune/demyelinating Guillain–Barré syndrome · Chronic inflammatory demyelinating polyneuropathy Other Alcoholic polyneuropathy peripheral nervous system navs: anat/histo/physio/dev, noncongen PNS somatic/autonomic/congen/neoplasia, symptoms+signs/eponymous, proc

v • d • e Diseases of myoneural junction and muscle / neuromuscular disease (G70-G73, 358-359) Neuromuscular- junction disease autoimmune (Myasthenia gravis, Lambert-Eaton myasthenic syndrome) Myopathy/ congenital myopathy Muscular dystrophy (DAPC) AD Limb-girdle muscular dystrophy 1 · Oculopharyngeal · Facioscapulohumeral · Myotonic · Distal (most) AR Limb-girdle muscular dystrophy 2 · Congenital (Fukuyama, Ullrich) XR dystrophin (Becker's, Duchenne) · Emerin Emery-Dreifuss Other structural collagen disease (Bethlem myopathy) · PTP disease (X-linked MTM) · adaptor protein disease (BIN1-linked centronuclear myopathy) · cytoskeleton disease (Nemaline myopathy, Zaspopathy) Channelopathy Myotonia Myotonia congenita · Thomsen disease · Neuromyotonia/Isaacs syndrome · Paramyotonia congenita Periodic paralysis Hypokalemic · Hyperkalemic Other Central core disease Mitochondrial myopathy MELAS · MERRF · KSS · PEO Other Inflammatory myopathy muscle, DF+DRCT navs: anat/hist/physio, acquired myopathy/congenital myopathy/neoplasia, symptoms+signs/eponymous, proc